由 ADAMTS13 检测工作组代表国际血液学标准化理事会（ICSH）编写的指南文件，该工作组由临床与实验室专家组成的国际团队构成。本文件就临床实验室开展 ADAMTS13 检测的最佳实践提出建议，此类检测支持血栓性微血管病的鉴别诊断，并有助于血栓性血小板减少性紫癜（TTP）的管理。
Guidance document prepared on behalf of the International Council for Standardization in Haematology (ICSH), by the ADAMTS13 Assay Working Group, which comprises an international group of both clinical and laboratory experts. The document provides recommendations on best practice for the performance of ADAMTS13 assays in clinical laboratories that support the differential diagnosis of thrombotic microangiopathies and have utility in the management of thrombotic thrombocytopenic purpura (TTP).